Two Cases of Goldenhar's Syndrome Associated with the Narrowing of Internal Auditory Canal
내이도 협착을 동반한 Goldenhar증후군 2예
박, 기현; 정, 연훈; 김, 병철
Taehan Ibi Inhukwa Hakhoe chi, 44(4):427-430, 2001
Taehan Ibi Inhukwa Hakhoe chi; Journal of the Korean Otolaryngological Society; 대한이비인후과학회지
Goldenhar's syndrome is an association of symptoms such as epibulbar dermoids, preauricular appendages or pretragal fistulas, and mandibulo-facial dystosis. The disting uishing feature, therefore, is the underdevelopment of one half of the face.
Sensorinerual hearing loss and conductive hearing loss is associated with this syndrome. Facial paralysis has been reported to occur in patients with Goldenhar's syndrome. It was suggested that a pathologically narrow internal auditory canal may
indicate a failure of facial nerve development and that hypoplasia of facial nerve may result in facial paralysis. Furthermore, hypoplasia of acoustic nerve may result in sensorinerual hearing loss. In this report, we present two patients with
Goldenhar's syndrome, and suggest that the defects in acoustic and facial nerve function might be closely related to the narrowing of the internal auditory canal.
Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.
Total Visit :2,916,668
Total Download :1,178,557
Today View :96
Ajou University Medical Information & Media Center 164 Worldcup-ro Yeongtong-gu Suwon 16499 Korea / TEL : 031-219-5312 / FAX : 031-219-5314 Copyright (c) Ajou University Medical Information & Media Center All Rights Reserved. AJOU Open Repository는 국립중앙도서관 OAK 보급사업으로 구축되었습니다.