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Auxiliary partial orthotopic living donor liver transplantation in a patient with Wilson's disease: a case report.

Authors
Park, YK; Kim, BW; Wang, HJ; Kim, MW
Citation
Transplantation proceedings, 40(10):3808-3809, 2008
Journal Title
Transplantation proceedings
ISSN
0041-13451873-2623
Abstract
A patient with end-stage liver cirrhosis and neurological disorder due to Wilson's disease (WD) underwent auxiliary partial orthotopic liver transplantation (APOLT) using a living donor. He first visited our institute complaining of hand tremor, which was diagnosed as WD. Despite medical therapy, hepatic impairment progressed toward portal hypertensive complications. He was considered a suitable candidate for living donor-related liver transplantation. However, because of the impossibility of mobilization of the lateral section due to severe splenomegaly at the time of the recipient operation, we performed an APOLT using a right lobe graft. After transplantation, he suffered hepatic vein stenosis and biliary stenosis, receiving interventional therapy. The remnant native liver volume decreased, and the volume of the graft increased serially after transplantation. At the time of reporting, the patient had a normal working life with normal serum ceruloplasmin level and without neurologic problems at 26 months posttransplantation. APOLT may be a therapeutic option for patients with WD.
MeSH terms
AdultCeruloplasmin/metabolismCryopreservationHepatic Veins/surgeryHepatolenticular Degeneration/complicationsHepatolenticular Degeneration/surgeryHumansIliac Vein/surgeryLiver Cirrhosis/etiologyLiver Cirrhosis/surgery*Liver Transplantation/methods*Living Donors*MaleSiblingsTreatment OutcomeTremor/etiology
DOI
10.1016/j.transproceed.2008.07.128
PMID
19100498
Appears in Collections:
Journal Papers > School of Medicine / Graduate School of Medicine > Surgery
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